Oral findings in Alagille syndrome. A case report.

نویسندگان

  • Sabeeha Al-Mutawa
  • Bapsy Mathews
  • Nathanael Salako
چکیده

OBJECTIVE To highlight the role of dental practitioners in the management of children with liver diseases. CLINICAL PRESENTATION A 13-year-old girl with Alagille syndrome presented with oral manifestation of end-stage liver disease that needed liver transplant. The dentition showed hypoplastic lesions and severe discoloration. The gingiva was inflamed and edematous due to poor oral hygiene and possibly to the medication the child was placed on to reduce graft rejection. CONCLUSION Dental considerations should be incorporated in the overall management of children with liver disease and transplant. Consultation with a dental practitioner should be sought before, during and after treatment of such cases.

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عنوان ژورنال:
  • Medical principles and practice : international journal of the Kuwait University, Health Science Centre

دوره 11 3  شماره 

صفحات  -

تاریخ انتشار 2002